1. Q44 Congenital malformations of gallbladder, bile ducts and liver

    1. Q44.0 Agenesis, aplasia and hypoplasia of gallbladder

      Inclusion term(s):

      • Congenital absence of gallbladder
    2. Q44.1 Other congenital malformations of gallbladder

      Inclusion term(s):

      • Congenital malformation of gallbladder NOS
      • Intrahepatic gallbladder
    3. Q44.2 Atresia of bile ducts

    4. Q44.3 Congenital stenosis and stricture of bile ducts

    5. Q44.4 Choledochal cyst

    6. Q44.5 Other congenital malformations of bile ducts

      Inclusion term(s):

      • Accessory hepatic duct
      • Biliary duct duplication
      • Congenital malformation of bile duct NOS
      • Cystic duct duplication
    7. Q44.6 Cystic disease of liver

      Inclusion term(s):

      • Fibrocystic disease of liver
    8. Q44.7 Other congenital malformations of liver

      1. Q44.70 Other congenital malformation of liver, unspecified

        Inclusion term(s):

        • Congenital malformation of liver, NOS
      2. Q44.71 Alagille syndrome

        Inclusion term(s):

        • Alagille-Watson syndrome
      3. Q44.79 Other congenital malformations of liver

        Inclusion term(s):

        • Accessory liver
        • Congenital absence of liver
        • Congenital hepatomegaly
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.