1. D55 Anemia due to enzyme disorders

    1. D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency

      Inclusion term(s):

      • Favism
      • G6PD deficiency anemia
    2. D55.1 Anemia due to other disorders of glutathione metabolism

      Inclusion term(s):

      • Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
      • Anemia (due to) hemolytic nonspherocytic (hereditary), type I
    3. D55.2 Anemia due to disorders of glycolytic enzymes

      1. D55.21 Anemia due to pyruvate kinase deficiency

        Inclusion term(s):

        • PK deficiency anemia
        • Pyruvate kinase deficiency anemia
      2. D55.29 Anemia due to other disorders of glycolytic enzymes

        Inclusion term(s):

        • Hexokinase deficiency anemia
        • Triose-phosphate isomerase deficiency anemia
    4. D55.3 Anemia due to disorders of nucleotide metabolism

    5. D55.8 Other anemias due to enzyme disorders

    6. D55.9 Anemia due to enzyme disorder, unspecified

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.