Includes:

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes1

  • autoimmune disease (systemic) NOS (M35.9)
  • functional disorders of polymorphonuclear neutrophils (D71)
  • human immunodeficiency virus [HIV] disease (B20)
  1. D86 Sarcoidosis

    1. D86.0 Sarcoidosis of lung

    2. D86.1 Sarcoidosis of lymph nodes

    3. D86.2 Sarcoidosis of lung with sarcoidosis of lymph nodes

    4. D86.3 Sarcoidosis of skin

    5. D86.8 Sarcoidosis of other sites

      1. D86.81 Sarcoid meningitis

      2. D86.82 Multiple cranial nerve palsies in sarcoidosis

      3. D86.83 Sarcoid iridocyclitis

      4. D86.84 Sarcoid pyelonephritis

        Inclusion term(s):

        • Tubulo-interstitial nephropathy in sarcoidosis
      5. D86.85 Sarcoid myocarditis

      6. D86.86 Sarcoid arthropathy

        Inclusion term(s):

        • Polyarthritis in sarcoidosis
      7. D86.87 Sarcoid myositis

      8. D86.89 Sarcoidosis of other sites

        Inclusion term(s):

        • Hepatic granuloma
        • Uveoparotid fever [Heerfordt]
    6. D86.9 Sarcoidosis, unspecified

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.