1. G90 Disorders of autonomic nervous system

    Excludes1

    • dysfunction of the autonomic nervous system due to alcohol (G31.2)
    1. G90.0 Idiopathic peripheral autonomic neuropathy

      1. G90.01 Carotid sinus syncope

        Inclusion term(s):

        • Carotid sinus syndrome
      2. G90.09 Other idiopathic peripheral autonomic neuropathy

        Inclusion term(s):

        • Idiopathic peripheral autonomic neuropathy NOS
    2. G90.1 Familial dysautonomia [Riley-Day]

    3. G90.2 Horner's syndrome

      Inclusion term(s):

      • Bernard(-Horner) syndrome
      • Cervical sympathetic dystrophy or paralysis
    4. G90.3 Multi-system degeneration of the autonomic nervous system

      Inclusion term(s):

      • Neurogenic orthostatic hypotension [Shy-Drager]
    5. G90.4 Autonomic dysreflexia

    6. G90.5 Complex regional pain syndrome I (CRPS I)

      Inclusion term(s):

      • Reflex sympathetic dystrophy
      1. G90.50 Complex regional pain syndrome I, unspecified

      2. G90.51 Complex regional pain syndrome I of upper limb

        • G90.511 Complex regional pain syndrome I of right upper limb
        • G90.512 Complex regional pain syndrome I of left upper limb
        • G90.513 Complex regional pain syndrome I of upper limb, bilateral
        • G90.519 Complex regional pain syndrome I of unspecified upper limb
      3. G90.52 Complex regional pain syndrome I of lower limb

        • G90.521 Complex regional pain syndrome I of right lower limb
        • G90.522 Complex regional pain syndrome I of left lower limb
        • G90.523 Complex regional pain syndrome I of lower limb, bilateral
        • G90.529 Complex regional pain syndrome I of unspecified lower limb
      4. G90.59 Complex regional pain syndrome I of other specified site

    7. G90.8 Other disorders of autonomic nervous system

    8. G90.9 Disorder of the autonomic nervous system, unspecified

    9. G90.A Postural orthostatic tachycardia syndrome [POTS]

      Inclusion term(s):

      • Chronic orthostatic intolerance
      • Postural tachycardia syndrome
    10. G90.B LMNB1-related autosomal dominant leukodystrophy

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.