1. I27 Other pulmonary heart diseases

    1. I27.0 Primary pulmonary hypertension

      Inclusion term(s):

      • Heritable pulmonary arterial hypertension
      • Idiopathic pulmonary arterial hypertension
      • Primary group 1 pulmonary hypertension
      • Primary pulmonary arterial hypertension
    2. I27.1 Kyphoscoliotic heart disease

    3. I27.2 Other secondary pulmonary hypertension

      1. I27.20 Pulmonary hypertension, unspecified

        Inclusion term(s):

        • Pulmonary hypertension NOS
      2. I27.21 Secondary pulmonary arterial hypertension

        Inclusion term(s):

        • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
        • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
      3. I27.22 Pulmonary hypertension due to left heart disease

        Inclusion term(s):

        • Group 2 pulmonary hypertension
      4. I27.23 Pulmonary hypertension due to lung diseases and hypoxia

        Inclusion term(s):

        • Group 3 pulmonary hypertension
      5. I27.24 Chronic thromboembolic pulmonary hypertension

        Inclusion term(s):

        • Group 4 pulmonary hypertension
      6. I27.29 Other secondary pulmonary hypertension

        Inclusion term(s):

        • Group 5 pulmonary hypertension
        • Pulmonary hypertension with unclear multifactorial mechanisms
        • Pulmonary hypertension due to hematologic disorders
        • Pulmonary hypertension due to metabolic disorders
        • Pulmonary hypertension due to other systemic disorders
    4. I27.8 Other specified pulmonary heart diseases

      1. I27.81 Cor pulmonale (chronic)

        Inclusion term(s):

        • Cor pulmonale NOS
      2. I27.82 Chronic pulmonary embolism

      3. I27.83 Eisenmenger's syndrome

        Inclusion term(s):

        • Eisenmenger's complex
        • (Irreversible) Eisenmenger's disease
        • Pulmonary hypertension with right to left shunt related to congenital heart disease
      4. I27.89 Other specified pulmonary heart diseases

    5. I27.9 Pulmonary heart disease, unspecified

      Inclusion term(s):

      • Chronic cardiopulmonary disease
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.