• postpolio syndrome (G14)
  • sequelae of poliomyelitis (B91)
  • sequelae of viral encephalitis (B94.1)
  1. A81 Atypical virus infections of central nervous system

    Use additional code, if applicable, to identify:
    dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
    dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
    dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
    dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
    dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
    mild neurocognitive disorder due to known physiological condition (F06.7-)


    • diseases of the central nervous system caused by prions
    1. A81.0 Creutzfeldt-Jakob disease

      1. A81.00 Creutzfeldt-Jakob disease, unspecified

        Inclusion term(s):

        • Jakob-Creutzfeldt disease, unspecified
      2. A81.01 Variant Creutzfeldt-Jakob disease

        Inclusion term(s):

        • vCJD
      3. A81.09 Other Creutzfeldt-Jakob disease

        Inclusion term(s):

        • CJD
        • Familial Creutzfeldt-Jakob disease
        • Iatrogenic Creutzfeldt-Jakob disease
        • Sporadic Creutzfeldt-Jakob disease
        • Subacute spongiform encephalopathy (with dementia)
    2. A81.1 Subacute sclerosing panencephalitis

      Inclusion term(s):

      • Dawson's inclusion body encephalitis
      • Van Bogaert's sclerosing leukoencephalopathy
    3. A81.2 Progressive multifocal leukoencephalopathy

      Inclusion term(s):

      • Multifocal leukoencephalopathy NOS
    4. A81.8 Other atypical virus infections of central nervous system

      1. A81.81 Kuru

      2. A81.82 Gerstmann-Sträussler-Scheinker syndrome

        Inclusion term(s):

        • GSS syndrome
      3. A81.83 Fatal familial insomnia

        Inclusion term(s):

        • FFI
      4. A81.89 Other atypical virus infections of central nervous system

    5. A81.9 Atypical virus infection of central nervous system, unspecified

      Inclusion term(s):

      • Prion diseases of the central nervous system NOS
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.