Excludes1

  • postpolio syndrome (G14)
  • sequelae of poliomyelitis (B91)
  • sequelae of viral encephalitis (B94.1)
  1. A81 Atypical virus infections of central nervous system

    Use Additional code to identify:
    dementia with behavioral disturbance (F02.81)
    dementia without behavioral disturbance (F02.80)

    Includes:

    • diseases of the central nervous system caused by prions
    1. A81.0 Creutzfeldt-Jakob disease

      1. A81.00 Creutzfeldt-Jakob disease, unspecified

        Inclusion term(s):

        • Jakob-Creutzfeldt disease, unspecified
      2. A81.01 Variant Creutzfeldt-Jakob disease

        Inclusion term(s):

        • vCJD
      3. A81.09 Other Creutzfeldt-Jakob disease

        Inclusion term(s):

        • CJD
        • Familial Creutzfeldt-Jakob disease
        • Iatrogenic Creutzfeldt-Jakob disease
        • Sporadic Creutzfeldt-Jakob disease
        • Subacute spongiform encephalopathy (with dementia)
    2. A81.1 Subacute sclerosing panencephalitis

      Inclusion term(s):

      • Dawson's inclusion body encephalitis
      • Van Bogaert's sclerosing leukoencephalopathy
    3. A81.2 Progressive multifocal leukoencephalopathy

      Inclusion term(s):

      • Multifocal leukoencephalopathy NOS
    4. A81.8 Other atypical virus infections of central nervous system

      1. A81.81 Kuru

      2. A81.82 Gerstmann-Sträussler-Scheinker syndrome

        Inclusion term(s):

        • GSS syndrome
      3. A81.83 Fatal familial insomnia

        Inclusion term(s):

        • FFI
      4. A81.89 Other atypical virus infections of central nervous system

    5. A81.9 Atypical virus infection of central nervous system, unspecified

      Inclusion term(s):

      • Prion diseases of the central nervous system NOS
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.