Excludes2

  • Kaposi's sarcoma of lymph nodes (C46.3)
  • secondary and unspecified neoplasm of lymph nodes (C77.-)
  • secondary neoplasm of bone marrow (C79.52)
  • secondary neoplasm of spleen (C78.89)
  1. C91 Lymphoid leukemia

    Excludes1

    • personal history of leukemia (Z85.6)
    1. C91.0 Acute lymphoblastic leukemia [ALL]

      Note: Code C91.0 should only be used for T-cell and B-cell precursor leukemia

      1. C91.00 Acute lymphoblastic leukemia not having achieved remission

        Inclusion term(s):

        • Acute lymphoblastic leukemia with failed remission
        • Acute lymphoblastic leukemia NOS
      2. C91.01 Acute lymphoblastic leukemia, in remission

      3. C91.02 Acute lymphoblastic leukemia, in relapse

    2. C91.1 Chronic lymphocytic leukemia of B-cell type

      Inclusion term(s):

      • Lymphoplasmacytic leukemia
      • Richter syndrome
      1. C91.10 Chronic lymphocytic leukemia of B-cell type not having achieved remission

        Inclusion term(s):

        • Chronic lymphocytic leukemia of B-cell type with failed remission
        • Chronic lymphocytic leukemia of B-cell type NOS
      2. C91.11 Chronic lymphocytic leukemia of B-cell type in remission

      3. C91.12 Chronic lymphocytic leukemia of B-cell type in relapse

    3. C91.3 Prolymphocytic leukemia of B-cell type

      1. C91.30 Prolymphocytic leukemia of B-cell type not having achieved remission

        Inclusion term(s):

        • Prolymphocytic leukemia of B-cell type with failed remission
        • Prolymphocytic leukemia of B-cell type NOS
      2. C91.31 Prolymphocytic leukemia of B-cell type, in remission

      3. C91.32 Prolymphocytic leukemia of B-cell type, in relapse

    4. C91.4 Hairy cell leukemia

      Inclusion term(s):

      • Leukemic reticuloendotheliosis
      1. C91.40 Hairy cell leukemia not having achieved remission

        Inclusion term(s):

        • Hairy cell leukemia with failed remission
        • Hairy cell leukemia NOS
      2. C91.41 Hairy cell leukemia, in remission

      3. C91.42 Hairy cell leukemia, in relapse

    5. C91.5 Adult T-cell lymphoma/leukemia (HTLV-1-associated)

      Inclusion term(s):

      • Acute variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      • Chronic variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      • Lymphomatoid variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      • Smouldering variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      1. C91.50 Adult T-cell lymphoma/leukemia (HTLV-1-associated) not having achieved remission

        Inclusion term(s):

        • Adult T-cell lymphoma/leukemia (HTLV-1-associated) with failed remission
        • Adult T-cell lymphoma/leukemia (HTLV-1-associated) NOS
      2. C91.51 Adult T-cell lymphoma/leukemia (HTLV-1-associated), in remission

      3. C91.52 Adult T-cell lymphoma/leukemia (HTLV-1-associated), in relapse

    6. C91.6 Prolymphocytic leukemia of T-cell type

      1. C91.60 Prolymphocytic leukemia of T-cell type not having achieved remission

        Inclusion term(s):

        • Prolymphocytic leukemia of T-cell type with failed remission
        • Prolymphocytic leukemia of T-cell type NOS
      2. C91.61 Prolymphocytic leukemia of T-cell type, in remission

      3. C91.62 Prolymphocytic leukemia of T-cell type, in relapse

    7. C91.9 Lymphoid leukemia, unspecified

      1. C91.90 Lymphoid leukemia, unspecified not having achieved remission

        Inclusion term(s):

        • Lymphoid leukemia with failed remission
        • Lymphoid leukemia NOS
      2. C91.91 Lymphoid leukemia, unspecified, in remission

      3. C91.92 Lymphoid leukemia, unspecified, in relapse

    8. C91.A Mature B-cell leukemia Burkitt-type

      1. C91.A0 Mature B-cell leukemia Burkitt-type not having achieved remission

        Inclusion term(s):

        • Mature B-cell leukemia Burkitt-type with failed remission
        • Mature B-cell leukemia Burkitt-type NOS
      2. C91.A1 Mature B-cell leukemia Burkitt-type, in remission

      3. C91.A2 Mature B-cell leukemia Burkitt-type, in relapse

    9. C91.Z Other lymphoid leukemia

      Inclusion term(s):

      • T-cell large granular lymphocytic leukemia (associated with rheumatoid arthritis)
      1. C91.Z0 Other lymphoid leukemia not having achieved remission

        Inclusion term(s):

        • Other lymphoid leukemia with failed remission
        • Other lymphoid leukemia NOS
      2. C91.Z1 Other lymphoid leukemia, in remission

      3. C91.Z2 Other lymphoid leukemia, in relapse

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.