Categories D37-D44, and D48 classify by site neoplasms of uncertain behavior, i.e., histologic confirmation whether the neoplasm is malignant or benign cannot be made.

Excludes1

  • neoplasms of unspecified behavior (D49.-)
  1. D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

    1. D47.0 Mast cell neoplasms of uncertain behavior

      1. D47.01 Cutaneous mastocytosis

        Inclusion term(s):

        • Diffuse cutaneous mastocytosis
        • Maculopapular cutaneous mastocytosis
        • Solitary mastocytoma
        • Telangiectasia macularis eruptiva perstans
        • Urticaria pigmentosa
      2. D47.02 Systemic mastocytosis

        Inclusion term(s):

        • Indolent systemic mastocytosis
        • Isolated bone marrow mastocytosis
        • Smoldering systemic mastocytosis
        • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
      3. D47.09 Other mast cell neoplasms of uncertain behavior

        Inclusion term(s):

        • Extracutaneous mastocytoma
        • Mast cell tumor NOS
        • Mastocytoma NOS
        • Mastocytosis NOS
    2. D47.1 Chronic myeloproliferative disease

      Inclusion term(s):

      • Chronic neutrophilic leukemia
      • Myeloproliferative disease, unspecified
    3. D47.2 Monoclonal gammopathy

      Inclusion term(s):

      • Monoclonal gammopathy of undetermined significance [MGUS]
    4. D47.3 Essential (hemorrhagic) thrombocythemia

      Inclusion term(s):

      • Essential thrombocytosis
      • Idiopathic hemorrhagic thrombocythemia
    5. D47.4 Osteomyelofibrosis

      Inclusion term(s):

      • Chronic idiopathic myelofibrosis
      • Myelofibrosis (idiopathic) (with myeloid metaplasia)
      • Myelosclerosis (megakaryocytic) with myeloid metaplasia
      • Secondary myelofibrosis in myeloproliferative disease
    6. D47.9 Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified

      Inclusion term(s):

      • Lymphoproliferative disease NOS
    7. D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

      1. D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)

      2. D47.Z2 Castleman disease

      3. D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

        Inclusion term(s):

        • Histiocytic tumors of uncertain behavior
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.