1. D68 Other coagulation defects

    Excludes1

    • abnormal coagulation profile (R79.1)
    • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
    • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
    1. D68.0 Von Willebrand's disease

      Inclusion term(s):

      • Angiohemophilia
      • Factor VIII deficiency with vascular defect
      • Vascular hemophilia
    2. D68.1 Hereditary factor XI deficiency

      Inclusion term(s):

      • Hemophilia C
      • Plasma thromboplastin antecedent [PTA] deficiency
      • Rosenthal's disease
    3. D68.2 Hereditary deficiency of other clotting factors

      Inclusion term(s):

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    4. D68.3 Hemorrhagic disorder due to circulating anticoagulants

      1. D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors

        • D68.311 Acquired hemophilia

          Inclusion term(s):

          • Autoimmune hemophilia
          • Autoimmune inhibitors to clotting factors
          • Secondary hemophilia
        • D68.312 Antiphospholipid antibody with hemorrhagic disorder

          Inclusion term(s):

          • Lupus anticoagulant (LAC) with hemorrhagic disorder
          • Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder
        • D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors

          Inclusion term(s):

          • Antithromboplastinemia
          • Antithromboplastinogenemia
          • Hemorrhagic disorder due to intrinsic increase in antithrombin
          • Hemorrhagic disorder due to intrinsic increase in anti-VIIIa
          • Hemorrhagic disorder due to intrinsic increase in anti-IXa
          • Hemorrhagic disorder due to intrinsic increase in anti-XIa
      2. D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants

        Inclusion term(s):

        • Drug-induced hemorrhagic disorder
        • Hemorrhagic disorder due to increase in anti-IIa
        • Hemorrhagic disorder due to increase in anti-Xa
        • Hyperheparinemia
    5. D68.4 Acquired coagulation factor deficiency

      Inclusion term(s):

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency
    6. D68.5 Primary thrombophilia

      Inclusion term(s):

      • Primary hypercoagulable states
      1. D68.51 Activated protein C resistance

        Inclusion term(s):

        • Factor V Leiden mutation
      2. D68.52 Prothrombin gene mutation

      3. D68.59 Other primary thrombophilia

        Inclusion term(s):

        • Antithrombin III deficiency
        • Hypercoagulable state NOS
        • Primary hypercoagulable state NEC
        • Primary thrombophilia NEC
        • Protein C deficiency
        • Protein S deficiency
        • Thrombophilia NOS
    7. D68.6 Other thrombophilia

      Inclusion term(s):

      • Other hypercoagulable states
      1. D68.61 Antiphospholipid syndrome

        Inclusion term(s):

        • Anticardiolipin syndrome
        • Antiphospholipid antibody syndrome
      2. D68.62 Lupus anticoagulant syndrome

        Inclusion term(s):

        • Lupus anticoagulant
        • Presence of systemic lupus erythematosus [SLE] inhibitor
      3. D68.69 Other thrombophilia

        Inclusion term(s):

        • Hypercoagulable states NEC
        • Secondary hypercoagulable state NOS
    8. D68.8 Other specified coagulation defects

    9. D68.9 Coagulation defect, unspecified

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.