1. D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue


    • (Abt-) Letterer-Siwe disease (C96.0)
    • eosinophilic granuloma (C96.6)
    • Hand-Schüller-Christian disease (C96.5)
    • histiocytic medullary reticulosis (C96.9)
    • histiocytic sarcoma (C96.A)
    • histiocytosis X, multifocal (C96.5)
    • histiocytosis X, unifocal (C96.6)
    • Langerhans-cell histiocytosis, multifocal (C96.5)
    • Langerhans-cell histiocytosis NOS (C96.6)
    • Langerhans-cell histiocytosis, unifocal (C96.6)
    • leukemic reticuloendotheliosis (C91.4-)
    • lipomelanotic reticulosis (I89.8)
    • malignant histiocytosis (C96.A)
    • malignant reticulosis (C86.0)
    • nonlipid reticuloendotheliosis (C96.0)
    1. D76.1 Hemophagocytic lymphohistiocytosis

      Inclusion term(s):

      • Familial hemophagocytic reticulosis
      • Histiocytoses of mononuclear phagocytes
    2. D76.2 Hemophagocytic syndrome, infection-associated

    3. D76.3 Other histiocytosis syndromes

      Inclusion term(s):

      • Reticulohistiocytoma (giant-cell)
      • Sinus histiocytosis with massive lymphadenopathy
      • Xanthogranuloma
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.