1. G11 Hereditary ataxia

    Excludes2

    • cerebral palsy (G80.-)
    • hereditary and idiopathic neuropathy (G60.-)
    • metabolic disorders (E70-E88)
    1. G11.0 Congenital nonprogressive ataxia

    2. G11.1 Early-onset cerebellar ataxia

      Inclusion term(s):

      • Early-onset cerebellar ataxia with essential tremor
      • Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
      • Early-onset cerebellar ataxia with retained tendon reflexes
      • Friedreich's ataxia (autosomal recessive)
      • X-linked recessive spinocerebellar ataxia
    3. G11.2 Late-onset cerebellar ataxia

    4. G11.3 Cerebellar ataxia with defective DNA repair

      Inclusion term(s):

      • Ataxia telangiectasia [Louis-Bar]
    5. G11.4 Hereditary spastic paraplegia

    6. G11.8 Other hereditary ataxias

    7. G11.9 Hereditary ataxia, unspecified

      Inclusion term(s):

      • Hereditary cerebellar ataxia NOS
      • Hereditary cerebellar degeneration
      • Hereditary cerebellar disease
      • Hereditary cerebellar syndrome
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.