1. G40 Epilepsy and recurrent seizures

    Note: the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled

    Excludes1

    • conversion disorder with seizures (F44.5)
    • convulsions NOS (R56.9)
    • post traumatic seizures (R56.1)
    • seizure (convulsive) NOS (R56.9)
    • seizure of newborn (P90)

    Excludes2

    1. G40.0 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset

      Inclusion term(s):

      • Benign childhood epilepsy with centrotemporal EEG spikes
      • Childhood epilepsy with occipital EEG paroxysms
      1. G40.00 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable

        Inclusion term(s):

        • Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset without intractability
        • G40.001 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus
        • G40.009 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus

          Inclusion term(s):

          • Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset NOS
      2. G40.01 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable

        • G40.011 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus
        • G40.019 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus
    2. G40.1 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures

      Inclusion term(s):

      • Attacks without alteration of consciousness
      • Epilepsia partialis continua [Kozhevnikof]
      • Simple partial seizures developing into secondarily generalized seizures
      1. G40.10 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable

        Inclusion term(s):

        • Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures without intractability
        • G40.101 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus
        • G40.109 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus

          Inclusion term(s):

          • Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures NOS
      2. G40.11 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable

        • G40.111 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus
        • G40.119 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus
    3. G40.2 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures

      Inclusion term(s):

      • Attacks with alteration of consciousness, often with automatisms
      • Complex partial seizures developing into secondarily generalized seizures
      1. G40.20 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable

        Inclusion term(s):

        • Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures without intractability
        • G40.201 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus
        • G40.209 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus

          Inclusion term(s):

          • Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures NOS
      2. G40.21 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable

        • G40.211 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus
        • G40.219 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus
    4. G40.3 Generalized idiopathic epilepsy and epileptic syndromes

      1. G40.30 Generalized idiopathic epilepsy and epileptic syndromes, not intractable

        Inclusion term(s):

        • Generalized idiopathic epilepsy and epileptic syndromes without intractability
        • G40.301 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus
        • G40.309 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus

          Inclusion term(s):

          • Generalized idiopathic epilepsy and epileptic syndromes NOS
      2. G40.31 Generalized idiopathic epilepsy and epileptic syndromes, intractable

        • G40.311 Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus
        • G40.319 Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus
    5. G40.4 Other generalized epilepsy and epileptic syndromes

      Inclusion term(s):

      • Epilepsy with grand mal seizures on awakening
      • Epilepsy with myoclonic absences
      • Epilepsy with myoclonic-astatic seizures
      • Grand mal seizure NOS
      • Nonspecific atonic epileptic seizures
      • Nonspecific clonic epileptic seizures
      • Nonspecific myoclonic epileptic seizures
      • Nonspecific tonic epileptic seizures
      • Nonspecific tonic-clonic epileptic seizures
      • Symptomatic early myoclonic encephalopathy
      1. G40.40 Other generalized epilepsy and epileptic syndromes, not intractable

        Inclusion term(s):

        • Other generalized epilepsy and epileptic syndromes without intractability
        • Other generalized epilepsy and epileptic syndromes NOS
        • G40.401 Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus
        • G40.409 Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus
      2. G40.41 Other generalized epilepsy and epileptic syndromes, intractable

        • G40.411 Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus
        • G40.419 Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus
      3. G40.42 Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

        Inclusion term(s):

        • CDKL5
    6. G40.5 Epileptic seizures related to external causes

      Inclusion term(s):

      • Epileptic seizures related to alcohol
      • Epileptic seizures related to drugs
      • Epileptic seizures related to hormonal changes
      • Epileptic seizures related to sleep deprivation
      • Epileptic seizures related to stress
      1. G40.50 Epileptic seizures related to external causes, not intractable

        • G40.501 Epileptic seizures related to external causes, not intractable, with status epilepticus
        • G40.509 Epileptic seizures related to external causes, not intractable, without status epilepticus

          Inclusion term(s):

          • Epileptic seizures related to external causes, NOS
    7. G40.8 Other epilepsy and recurrent seizures

      Inclusion term(s):

      • Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized
      • Landau-Kleffner syndrome
      1. G40.80 Other epilepsy

        • G40.801 Other epilepsy, not intractable, with status epilepticus

          Inclusion term(s):

          • Other epilepsy without intractability with status epilepticus
        • G40.802 Other epilepsy, not intractable, without status epilepticus

          Inclusion term(s):

          • Other epilepsy NOS
          • Other epilepsy without intractability without status epilepticus
        • G40.803 Other epilepsy, intractable, with status epilepticus
        • G40.804 Other epilepsy, intractable, without status epilepticus
      2. G40.81 Lennox-Gastaut syndrome

        • G40.811 Lennox-Gastaut syndrome, not intractable, with status epilepticus
        • G40.812 Lennox-Gastaut syndrome, not intractable, without status epilepticus
        • G40.813 Lennox-Gastaut syndrome, intractable, with status epilepticus
        • G40.814 Lennox-Gastaut syndrome, intractable, without status epilepticus
      3. G40.82 Epileptic spasms

        Inclusion term(s):

        • Infantile spasms
        • Salaam attacks
        • West's syndrome
        • G40.821 Epileptic spasms, not intractable, with status epilepticus
        • G40.822 Epileptic spasms, not intractable, without status epilepticus
        • G40.823 Epileptic spasms, intractable, with status epilepticus
        • G40.824 Epileptic spasms, intractable, without status epilepticus
      4. G40.83 Dravet syndrome

        Inclusion term(s):

        • Polymorphic epilepsy in infancy (PMEI)
        • Severe myoclonic epilepsy in infancy (SMEI)
        • G40.833 Dravet syndrome, intractable, with status epilepticus
        • G40.834 Dravet syndrome, intractable, without status epilepticus

          Inclusion term(s):

          • Dravet syndrome NOS
      5. G40.89 Other seizures

    8. G40.9 Epilepsy, unspecified

      1. G40.90 Epilepsy, unspecified, not intractable

        Inclusion term(s):

        • Epilepsy, unspecified, without intractability
        • G40.901 Epilepsy, unspecified, not intractable, with status epilepticus
        • G40.909 Epilepsy, unspecified, not intractable, without status epilepticus

          Inclusion term(s):

          • Epilepsy NOS
          • Epileptic convulsions NOS
          • Epileptic fits NOS
          • Epileptic seizures NOS
          • Recurrent seizures NOS
          • Seizure disorder NOS
      2. G40.91 Epilepsy, unspecified, intractable

        Inclusion term(s):

        • Intractable seizure disorder NOS
        • G40.911 Epilepsy, unspecified, intractable, with status epilepticus
        • G40.919 Epilepsy, unspecified, intractable, without status epilepticus
    9. G40.A Absence epileptic syndrome

      Inclusion term(s):

      • Childhood absence epilepsy [pyknolepsy]
      • Juvenile absence epilepsy
      • Absence epileptic syndrome, NOS
      1. G40.A0 Absence epileptic syndrome, not intractable

        • G40.A01 Absence epileptic syndrome, not intractable, with status epilepticus
        • G40.A09 Absence epileptic syndrome, not intractable, without status epilepticus
      2. G40.A1 Absence epileptic syndrome, intractable

        • G40.A11 Absence epileptic syndrome, intractable, with status epilepticus
        • G40.A19 Absence epileptic syndrome, intractable, without status epilepticus
    10. G40.B Juvenile myoclonic epilepsy [impulsive petit mal]

      1. G40.B0 Juvenile myoclonic epilepsy, not intractable

        • G40.B01 Juvenile myoclonic epilepsy, not intractable, with status epilepticus
        • G40.B09 Juvenile myoclonic epilepsy, not intractable, without status epilepticus
      2. G40.B1 Juvenile myoclonic epilepsy, intractable

        • G40.B11 Juvenile myoclonic epilepsy, intractable, with status epilepticus
        • G40.B19 Juvenile myoclonic epilepsy, intractable, without status epilepticus
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.