1. J84 Other interstitial pulmonary diseases

    Excludes1

    • drug-induced interstitial lung disorders (J70.2-J70.4)
    • interstitial emphysema (J98.2)

    Excludes2

    • lung diseases due to external agents (J60-J70)
    1. J84.0 Alveolar and parieto-alveolar conditions

      1. J84.01 Alveolar proteinosis

      2. J84.02 Pulmonary alveolar microlithiasis

      3. J84.03 Idiopathic pulmonary hemosiderosis

        Inclusion term(s):

        • Essential brown induration of lung
      4. J84.09 Other alveolar and parieto-alveolar conditions

    2. J84.1 Other interstitial pulmonary diseases with fibrosis

      1. J84.10 Pulmonary fibrosis, unspecified

        Inclusion term(s):

        • Capillary fibrosis of lung
        • Cirrhosis of lung (chronic) NOS
        • Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
        • Induration of lung (chronic) NOS
        • Postinflammatory pulmonary fibrosis
      2. J84.11 Idiopathic interstitial pneumonia

        • J84.111 Idiopathic interstitial pneumonia, not otherwise specified
        • J84.112 Idiopathic pulmonary fibrosis

          Inclusion term(s):

          • Cryptogenic fibrosing alveolitis
          • Idiopathic fibrosing alveolitis
        • J84.113 Idiopathic non-specific interstitial pneumonitis
        • J84.114 Acute interstitial pneumonitis

          Inclusion term(s):

          • Hamman-Rich syndrome
        • J84.115 Respiratory bronchiolitis interstitial lung disease
        • J84.116 Cryptogenic organizing pneumonia
        • J84.117 Desquamative interstitial pneumonia
      3. J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

        Inclusion term(s):

        • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
        • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
        • Organizing pneumonia due to collagen vascular disease
        • Organizing pneumonia in diseases classified elsewhere
    3. J84.2 Lymphoid interstitial pneumonia

      Inclusion term(s):

      • Lymphoid interstitial pneumonitis
    4. J84.8 Other specified interstitial pulmonary diseases

      1. J84.81 Lymphangioleiomyomatosis

        Inclusion term(s):

        • Lymphangiomyomatosis
      2. J84.82 Adult pulmonary Langerhans cell histiocytosis

        Inclusion term(s):

        • Adult PLCH
      3. J84.83 Surfactant mutations of the lung

      4. J84.84 Other interstitial lung diseases of childhood

        • J84.841 Neuroendocrine cell hyperplasia of infancy
        • J84.842 Pulmonary interstitial glycogenosis
        • J84.843 Alveolar capillary dysplasia with vein misalignment
        • J84.848 Other interstitial lung diseases of childhood
      5. J84.89 Other specified interstitial pulmonary diseases

        Inclusion term(s):

        • Endogenous lipoid pneumonia
        • Interstitial pneumonitis
        • Non-specific interstitial pneumonitis NOS
        • Organizing pneumonia NOS
    5. J84.9 Interstitial pulmonary disease, unspecified

      Inclusion term(s):

      • Interstitial pneumonia NOS
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.