• autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease


  • autoimmune disease, single organ or single cell-type -code to relevant condition category
  1. M30 Polyarteritis nodosa and related conditions


    • microscopic polyarteritis (M31.7)
    1. M30.0 Polyarteritis nodosa

    2. M30.1 Polyarteritis with lung involvement [Churg-Strauss]

      Inclusion term(s):

      • Allergic granulomatous angiitis
      • Eosinophilic granulomatosis with polyangiitis [EGPA]
    3. M30.2 Juvenile polyarteritis

    4. M30.3 Mucocutaneous lymph node syndrome [Kawasaki]

    5. M30.8 Other conditions related to polyarteritis nodosa

      Inclusion term(s):

      • Polyangiitis overlap syndrome
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.