• autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease


  • autoimmune disease, single organ or single cell-type -code to relevant condition category
  1. M31 Other necrotizing vasculopathies

    1. M31.0 Hypersensitivity angiitis

      Inclusion term(s):

      • Goodpasture's syndrome
    2. M31.1 Thrombotic microangiopathy

      1. M31.10 Thrombotic microangiopathy, unspecified

      2. M31.11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]

        Inclusion term(s):

        • Transplant-associated thrombotic microangiopathy [TA-TMA]
      3. M31.19 Other thrombotic microangiopathy

        Inclusion term(s):

        • Thrombotic thrombocytopenic purpura
    3. M31.2 Lethal midline granuloma

    4. M31.3 Wegener's granulomatosis

      Inclusion term(s):

      • Granulomatosis with polyangiitis
      • Necrotizing respiratory granulomatosis
      1. M31.30 Wegener's granulomatosis without renal involvement

        Inclusion term(s):

        • Wegener's granulomatosis NOS
      2. M31.31 Wegener's granulomatosis with renal involvement

    5. M31.4 Aortic arch syndrome [Takayasu]

    6. M31.5 Giant cell arteritis with polymyalgia rheumatica

    7. M31.6 Other giant cell arteritis

    8. M31.7 Microscopic polyangiitis

      Inclusion term(s):

      • Microscopic polyarteritis
    9. M31.8 Other specified necrotizing vasculopathies

      Inclusion term(s):

      • Hypocomplementemic vasculitis
      • Septic vasculitis
    10. M31.9 Necrotizing vasculopathy, unspecified

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.