• autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease


  • autoimmune disease, single organ or single cell-type -code to relevant condition category
  1. M35 Other systemic involvement of connective tissue


    • reactive perforating collagenosis (L87.1)
    1. M35.0 Sicca syndrome [Sjögren]

      1. M35.00 Sicca syndrome, unspecified

      2. M35.01 Sicca syndrome with keratoconjunctivitis

      3. M35.02 Sicca syndrome with lung involvement

      4. M35.03 Sicca syndrome with myopathy

      5. M35.04 Sicca syndrome with tubulo-interstitial nephropathy

        Inclusion term(s):

        • Renal tubular acidosis in sicca syndrome
      6. M35.09 Sicca syndrome with other organ involvement

    2. M35.1 Other overlap syndromes

      Inclusion term(s):

      • Mixed connective tissue disease
    3. M35.2 Behçet's disease

    4. M35.3 Polymyalgia rheumatica

    5. M35.4 Diffuse (eosinophilic) fasciitis

    6. M35.5 Multifocal fibrosclerosis

    7. M35.6 Relapsing panniculitis [Weber-Christian]

    8. M35.7 Hypermobility syndrome

      Inclusion term(s):

      • Familial ligamentous laxity
    9. M35.8 Other specified systemic involvement of connective tissue

    10. M35.9 Systemic involvement of connective tissue, unspecified

      Inclusion term(s):

      • Autoimmune disease (systemic) NOS
      • Collagen (vascular) disease NOS
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.