• autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease


  • autoimmune disease, single organ or single cell-type -code to relevant condition category
  1. M35 Other systemic involvement of connective tissue


    • reactive perforating collagenosis (L87.1)
    1. M35.0 Sjögren syndrome

      Inclusion term(s):

      • Sicca syndrome
      1. M35.00 Sjögren syndrome, unspecified

      2. M35.01 Sjögren syndrome with keratoconjunctivitis

      3. M35.02 Sjögren syndrome with lung involvement

      4. M35.03 Sjögren syndrome with myopathy

      5. M35.04 Sjögren syndrome with tubulo-interstitial nephropathy

        Inclusion term(s):

        • Renal tubular acidosis in sicca syndrome
      6. M35.05 Sjögren syndrome with inflammatory arthritis

      7. M35.06 Sjögren syndrome with peripheral nervous system involvement

      8. M35.07 Sjögren syndrome with central nervous system involvement

      9. M35.08 Sjögren syndrome with gastrointestinal involvement

      10. M35.09 Sjögren syndrome with other organ involvement

      11. M35.0A Sjögren syndrome with glomerular disease

      12. M35.0B Sjögren syndrome with vasculitis

      13. M35.0C Sjögren syndrome with dental involvement

    2. M35.1 Other overlap syndromes

      Inclusion term(s):

      • Mixed connective tissue disease
    3. M35.2 Behçet's disease

    4. M35.3 Polymyalgia rheumatica

    5. M35.4 Diffuse (eosinophilic) fasciitis

    6. M35.5 Multifocal fibrosclerosis

    7. M35.6 Relapsing panniculitis [Weber-Christian]

    8. M35.7 Hypermobility syndrome

      Inclusion term(s):

      • Familial ligamentous laxity
    9. M35.8 Other specified systemic involvement of connective tissue

      1. M35.81 Multisystem inflammatory syndrome

        Inclusion term(s):

        • MIS-A
        • MIS-C
        • Multisystem inflammatory syndrome in adults
        • Multisystem inflammatory syndrome in children
        • Pediatric inflammatory multisystem syndrome
        • PIMS
      2. M35.89 Other specified systemic involvement of connective tissue

    10. M35.9 Systemic involvement of connective tissue, unspecified

      Inclusion term(s):

      • Autoimmune disease (systemic) NOS
      • Collagen (vascular) disease NOS
Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.