1. Q82 Other congenital malformations of skin

    Excludes1

    • acrodermatitis enteropathica (E83.2)
    • congenital erythropoietic porphyria (E80.0)
    • pilonidal cyst or sinus (L05.-)
    • Sturge-Weber (-Dimitri) syndrome (Q85.8)
    1. Q82.0 Hereditary lymphedema

    2. Q82.1 Xeroderma pigmentosum

    3. Q82.2 Congenital cutaneous mastocytosis

      Inclusion term(s):

      • Congenital diffuse cutaneous mastocytosis
      • Congenital maculopapular cutaneous mastocytosis
      • Congenital urticaria pigmentosa
    4. Q82.3 Incontinentia pigmenti

    5. Q82.4 Ectodermal dysplasia (anhidrotic)

    6. Q82.5 Congenital non-neoplastic nevus

      Inclusion term(s):

      • Birthmark NOS
      • Flammeus Nevus
      • Portwine Nevus
      • Sanguineous Nevus
      • Strawberry Nevus
      • Vascular Nevus NOS
      • Verrucous Nevus
    7. Q82.6 Congenital sacral dimple

      Inclusion term(s):

      • Parasacral dimple
    8. Q82.8 Other specified congenital malformations of skin

      Inclusion term(s):

      • Abnormal palmar creases
      • Accessory skin tags
      • Benign familial pemphigus [Hailey-Hailey]
      • Congenital poikiloderma
      • Cutis laxa (hyperelastica)
      • Dermatoglyphic anomalies
      • Inherited keratosis palmaris et plantaris
      • Keratosis follicularis [Darier-White]
    9. Q82.9 Congenital malformation of skin, unspecified

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.