ICD-10 Code
International Classification of Diseases, 10th Revision
Feb 21, 2019
  ICD-10 Code for Lymphangioleiomyomatosis J84.81

J84.81 is a valid1 ICD 10 diagnosis code.

J84.81 is valid for submission for HIPAA-covered transactions.

Chapter 10 Diseases of the respiratory system (J00-J99)
Section J80-J84 Other respiratory diseases principally affecting the interstitium (J80-J84)
Category J84 Other interstitial pulmonary diseases

• See below for any additional coding requirements that may be necessary.

• Check for any notations, inclusions and/or exclusions that are specific to this ICD 10 code before using

1 No additional coding requirements necessary.
Inclusion Term
  • Lymphangiomyomatosis
See also ICD 10 code for

Related Terms to “Lymphangioleiomyomatosis”

  • Lymphangioleiomyomatosis - J84.81
  • Lymphangiomyomatosis - J84.81
See the ICD-10-CM Coding Guidelines.

Questions related to J84.81 Lymphangioleiomyomatosis

When ICD 10 was implemented on October 1, 2015, it did not affect physicians', outpatient facilities', and hospital outpatient departments' use of CPT codes on Medicare Fee-For-Service claims. Providers should continue to use CPT codes to report these services.