ICD-10 Code
International Classification of Diseases, 10th Revision
Mar 21, 2019

See: Disorders of copper metabolism

  ICD-10 Code for Wilson's disease E83.01

E83.01 is a valid1 ICD 10 diagnosis code.

E83.01 is valid for submission for HIPAA-covered transactions.

Chapter 4 Endocrine, nutritional and metabolic diseases (E00-E89)
Section E70-E88 Metabolic disorders (E70-E88)
Category E83 Disorders of mineral metabolism

• See below for any additional coding requirements that may be necessary.

• Check for any notations, inclusions and/or exclusions that are specific to this ICD 10 code before using

1 No additional coding requirements necessary.
Code Also
  • associated Kayser Fleischer ring (H18.04-)
See also ICD 10 code for

Related Terms to “Wilson's disease”

  • Cirrhosis, cirrhotic(hepatic) (liver) - K74.60
    • due to
      • hepatolenticular degeneration - E83.01
      • Wilson's disease - E83.01
  • Deficiency, deficient
    • ceruloplasmin(Wilson) - E83.01
  • Degeneration, degenerative
    • hepatolenticular(Wilson's) - E83.01
    • lenticular(familial) (progressive) (Wilson's) (with cirrhosis of liver) - E83.01
    • Wilson's hepatolenticular - E83.01
  • Dementia(degenerative (primary)) (old age) (persisting) - F03.90
    • in(due to)
      • hepatolenticular degeneration - E83.01
        • with behavioral disturbance - E83.01
  • Disease, diseasedSee also Syndrome
    • hepatolenticular - E83.01
    • Kinnier Wilson's(hepatolenticular degeneration) - E83.01
    • Wilson's(hepatolenticular degeneration) - E83.01
  • Disorder(of)See also Disease
  • Hepatolenticular degeneration - E83.01
  • Kinnier Wilson's disease(hepatolenticular degeneration) - E83.01
  • Lenticular degeneration, progressive - E83.01
  • Pseudosclerosis(brain)
    • of Westphal(Strümpell) - E83.01
  • PyelonephritisSee also Nephritis, tubulo-interstitial
    • in(due to)
      • Wilson's disease - E83.01
  • Strümpell-Westphal pseudosclerosis - E83.01
  • SyndromeSee also Disease
    • amyostatic(Wilson's disease) - E83.01
    • lenticular, progressive - E83.01
    • Westphal-Strümpell - E83.01
    • Wilson's(hepatolenticular degeneration) - E83.01
  • Westphal-Strümpell syndrome - E83.01
  • Wilson's
    • disease or syndrome - E83.01
    • hepatolenticular degeneration - E83.01
See the ICD-10-CM Coding Guidelines.

Questions related to E83.01 Wilson's disease

When ICD 10 was implemented on October 1, 2015, it did not affect physicians', outpatient facilities', and hospital outpatient departments' use of CPT codes on Medicare Fee-For-Service claims. Providers should continue to use CPT codes to report these services.