ICD-10 Code
International Classification of Diseases, 10th Revision
Aug 20, 2017
  ICD-10 Code for Lymphangioleiomyomatosis J84.81

J84.81 is a valid1 ICD 10 diagnosis code.

J84.81 is valid for submission for HIPAA-covered transactions.

Chapter 10 Diseases of the respiratory system (J00-J99)
Section J80-J84 Other respiratory diseases principally affecting the interstitium (J80-J84)
Category J84 Other interstitial pulmonary diseases

• See below for any additional coding requirements that may be necessary.

• Check for any notations, inclusions and/or exclusions that are specific to this ICD 10 code before using

1 No additional coding requirements necessary.
Inclusion Term
  • Lymphangiomyomatosis
See also ICD 10 code for

Related Terms to “Lymphangioleiomyomatosis”

  • Lymphangioleiomyomatosis - J84.81
  • Lymphangiomyomatosis - J84.81
See the 2017 ICD-10-CM Coding Guidelines.

When ICD 10 was implemented on October 1, 2015, it did not affect physicians', outpatient facilities', and hospital outpatient departments' use of CPT codes on Medicare Fee-For-Service claims. Providers should continue to use CPT codes to report these services.