Excludes2

  • Kaposi's sarcoma of lymph nodes (C46.3)
  • secondary and unspecified neoplasm of lymph nodes (C77.-)
  • secondary neoplasm of bone marrow (C79.52)
  • secondary neoplasm of spleen (C78.89)
  1. C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas

    Excludes1

    • B-cell lymphoma, unspecified (C85.1-)
    • personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79)
    1. C88.0 Waldenström macroglobulinemia

      Inclusion term(s):

      • Lymphoplasmacytic lymphoma with IgM-production
      • Macroglobulinemia (idiopathic) (primary)
      1. C88.00 Waldenström macroglobulinemia not having achieved remission

        Inclusion term(s):

        • Lymphoplasmacytic lymphoma with IgM-production, NOS
        • Lymphoplasmacytic lymphoma with IgM-production not having achieved remission
        • Lymphoplasmacytic lymphoma with IgM-production with failed remission
        • Macroglobulinemia (idiopathic) (primary) NOS
        • Macroglobulinemia (idiopathic) (primary) not having achieved remission
        • Macroglobulinemia (idiopathic) (primary) with failed remission
        • Waldenström macroglobulinemia NOS
        • Waldenström macroglobulinemia with failed remission
      2. C88.01 Waldenström macroglobulinemia, in remission

    2. C88.2 Heavy chain disease

      Inclusion term(s):

      • Franklin disease
      • Gamma heavy chain disease
      • Mu heavy chain disease
      1. C88.20 Heavy chain disease not having achieved remission

        Inclusion term(s):

        • Franklin disease NOS
        • Franklin disease not having achieved remission
        • Franklin disease with failed remission
        • Gamma heavy chain disease NOS
        • Gamma heavy chain disease not having achieved remission
        • Gamma heavy chain disease with failed remission
        • Heavy chain disease NOS
        • Heavy chain disease with failed remissionMu heavy chain disease not having achieved remission
        • Mu heavy chain disease NOS
        • Mu heavy chain disease not having achieved remission
        • Mu heavy chain disease with failed remission
      2. C88.21 Heavy chain disease, in remission

    3. C88.3 Immunoproliferative small intestinal disease

      Inclusion term(s):

      • Alpha heavy chain disease
      • Mediterranean lymphoma
      1. C88.30 Immunoproliferative small intestinal disease not having achieved remission

        Inclusion term(s):

        • Alpha heavy chain disease NOS
        • Alpha heavy chain disease not having achieved remission
        • Alpha heavy chain disease with failed remission
        • Immunoproliferative small intestinal disease NOS
        • Immunoproliferative small intestinal disease with failed remission
        • Mediterranean lymphoma NOS
        • Mediterranean lymphoma not having achieved remission
        • Mediterranean lymphoma with failed remission
      2. C88.31 Immunoproliferative small intestinal disease, in remission

    4. C88.4 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

      Inclusion term(s):

      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      1. C88.40 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

        Inclusion term(s):

        • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] NOS
        • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] with failed remission
        • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma] NOS
        • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma] not having achieved remission
        • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma] with failed remission
        • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma] NOS
        • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma] not having achieved remission
        • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma] with failed remission
      2. C88.41 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission

    5. C88.8 Other malignant immunoproliferative diseases

      1. C88.80 Other malignant immunoproliferative diseases not having achieved remission

        Inclusion term(s):

        • Other malignant immunoproliferative diseases NOS
        • Other malignant immunoproliferative diseases with failed remission
      2. C88.81 Other malignant immunoproliferative diseases, in remission

    6. C88.9 Malignant immunoproliferative disease, unspecified

      Inclusion term(s):

      • Immunoproliferative disease NOS
      1. C88.90 Malignant immunoproliferative disease, unspecified not having achieved remission

        Inclusion term(s):

        • Immunoproliferative disease NOS
        • Immunoproliferative disease NOS not having achieved remission
        • Immunoproliferative disease NOS with failed remission
        • Malignant immunoproliferative disease, unspecified NOS
        • Malignant immunoproliferative disease, unspecified with failed remission
      2. C88.91 Malignant immunoproliferative disease, unspecified, in remission

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.