Includes:

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes1

  • autoimmune disease (systemic) NOS (M35.9)
  • functional disorders of polymorphonuclear neutrophils (D71)
  • human immunodeficiency virus [HIV] disease (B20)
  1. D83 Common variable immunodeficiency

    1. D83.0 Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function

    2. D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders

    3. D83.2 Common variable immunodeficiency with autoantibodies to B- or T-cells

    4. D83.8 Other common variable immunodeficiencies

    5. D83.9 Common variable immunodeficiency, unspecified

Abbreviations used here:

NEC Not elsewhere classifiable
This abbreviation in the Tabular List represents “other specified”. When a specific code is not available for a condition, the Tabular List includes an NEC entry under a code to identify the code as the “other specified” code.

NOS Not otherwise specified
This abbreviation is the equivalent of unspecified.